A Pictorial Review of Immunoglobulin G4-related Sclerosing Disease
SM Yu, TKL Loke, JTH Yeung, WH Luk, LKM Wong
Hong Kong J Radiol 2014;17:208-17
DOI: 10.12809/hkjr1413200
Immunoglobulin (Ig) G4-related sclerosing disease is a relatively new disease entity. Any organ system can be affected. Therefore, there is a wide range of possible clinical manifestations. Diagnosis is often difficult and relies on a combination of radiological features, laboratory data, and histology findings. IgG4-related sclerosing diseases are frequently found to be associated with autoimmune pancreatitis. There are several established diagnostic criteria that are used to diagnose autoimmune pancreatitis. In our centre, we use the Asian Diagnostic Criteria for Autoimmune Pancreatitis in 2008. A total of 10 cases with proven IgG4-related systemic disease from 2008 to 2012 were reviewed. This pictorial essay aimed to share our imaging findings among patients with proven IgG4-related sclerosing disease.
中文摘要
免疫球蛋白G4相關性硬化病的圖文回顧
余燊明、陸國倫、楊芷珩、陸永恆、黃嘉敏
免疫球蛋白（Ig）G4相關性硬化病是一種較新的疾病。該病可以影響任何器官系統，所以可能的臨床表現形式多樣。診斷通常困難，需要綜合影像學特徵、實驗室數據和組織學結果。IgG4相關性硬化病通常與自身免疫性胰腺炎有關。目前已建立了診斷自身免疫性胰腺炎的幾套標準。我們中心使用自體免疫胰臟炎2008年亞洲診斷標準。本文圖文回顧2008至2012年確診為IgG4相關全身性疾病的10宗病例，旨在分享該病的影像學表現。