Lipoblastomatous Tumours, a Rare Entity: Report of Two Cases in Children

DD Rasalkar, WCW Chu

Hong Kong J Radiol 2010;13:209-12

Lipoblastomatous tumours are rare neoplasms derived from embryonic white adipose tissues. We report on two children with different types of lipoblastomatous tumours at rare sites. The first had a localised lipoblastoma within the peritoneal cavity, successfully resected without recurrence. The second patient had diffuse lipoblastomatosis infiltrating the paraspinal muscles and spinal canal, which recurred two years after surgery. Radiologically, both lesions had characteristic fat density signals. The former lesion was benign-looking with a well-defined border, while the latter was infiltrative and had raised the suspicion of malignant liposarcoma. The definitive diagnosis was derived from characteristic histopathological features.

中文摘要

罕見的脂肪母細胞腫瘤：兩個小兒病例

DD Rasalkar、朱昭穎

脂肪母細胞瘤是一種少見的腫瘤，源自於胎兒的白脂肪組織。本文報告兩名兒童的脂肪母細胞瘤發生在罕見位置。第一名兒童在腹膜腔處發現局限性脂肪母細胞瘤，經切除後未有復發。另一名兒童的瀰漫性脂肪母細胞瘤已滲入了脊旁肌及椎管，術後兩年復發。兩名兒童的病灶均出現脂肪密度的放射影像特徵。第一名兒童的病灶邊緣規則清晰，似乎屬良性。第二名兒童出現滲入性病灶，懷疑是惡性脂肪肉瘤。兩個病例均憑組織病理學特徵確診。