Posterior Cranial Fossa Neurenteric Cyst with Malignant Transformation

Full Article

JB Chiang, SSM Lo, LC Ho, CM Chan, WL Poon, KW Tang, YL Cheung

Hong Kong J Radiol 2014;17:281-4

DOI: 10.12809/hkjr1413223

Neurenteric cyst is a notably rare epithelium-lined cystic lesion found in the central nervous system. Malignant transformation of the neurenteric cyst is infrequent, with only six cases reported in the English literature. We report the case of a 74-year-old patient with recurrent neurenteric cyst in the posterior cranial fossa that underwent malignant transformation 2 years after initial surgery. Histologically, the initial lesion was compatible with benign neurenteric cyst, whereas the recurrent lesion illustrated features of adenocarcinoma.

 

中文摘要

後顱窩神經管原腸性囊腫的惡變

蔣碧茜、羅尚銘、何聯昌、陳智明、潘偉麟、鄧國穎、張毓靈

 

神經管原腸性囊腫是中樞神經系統一種特別罕見的上皮層囊性病變。神經管原腸性囊腫的惡變很少見,英文文獻中只報導了六個病例。本文報告一名74歲病人繼兩年前因神經管原腸性囊腫進行首次手術後,在後顱窩有惡性復發。組織學上,早期病變與良性神經管原腸性囊腫一致,但復發病灶有腺癌的特徵。