Infantile Intravesical Malignant Rhabdoid Tumour

Full Article

HKY Tam, A Li, PSF Lee, VPW Tse, KKY Pang

Hong Kong J Radiol 2013;16:e21-5

DOI: 10.12809/hkjr1312130

Malignant rhabdoid tumour is a rare, but highly aggressive, malignancy of early childhood. Malignant rhabdoid tumour can be classified according to renal and extrarenal locations. For extrarenal lesions, the spinal cord and central nervous system are most commonly involved, although such tumours may arise in almost any site. However, malignant rhabdoid tumour of the bladder has only been reported in a few patients, mainly focusing on its pathological aspects. We report on a patient with malignant rhabdoid tumour of the urinary bladder. The clinical, radiological, and histological features of this disease entity are discussed.

 

中文摘要

嬰兒膀胱惡性橫紋肌樣瘤

譚家盈、李子飛、李醒芬、謝佩溈、彭潔儀

惡性橫紋肌樣瘤是發生於童年早期的一種罕見、具高度侵襲性的惡性腫瘤。惡性橫紋肌樣瘤依據發病部位可分為腎內型和腎外型。儘管該腫瘤可發生於任何部位,但於腎外最常累及脊髓和中樞神經系統。然而,文獻中只有少數膀胱惡性橫紋肌樣瘤的病例,且主要集中於病理方面。本文報告一宗膀胱惡性橫紋肌樣瘤的病例,並討論相關臨床症狀、影像學及組織學特徵。